Paroxysmal nocturnal hemoglobinuria is a disease in which complement regulatory proteins are defective, so that activation of complement binding to red blood cells leads to episodes of spontaneous hemolysis.
La hemoglobinuria paroxística nocturna es una enfermedad en la que los reguladores del complemento están defectuosos, por lo que la activación del complemento que se une a los glóbulos rojos conduce a episodios de hemólisis espontánea.
Front | A disease in which complement regulatory proteins are defective, so that activation of complement binding to red blood cells leads to episodes of spontaneous hemolysis |
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Back | paroxysmal nocturnal hemoglobinuria |
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