Front | What is a medulloepithelioma? |
---|---|
Back | ● Rare tumor of nonpigmented epithelium of the ciliary body
● Neuroepithelial cell derived from primitive medullary epithelium
(inner layer of optic cup)
● Usually presents in children age 4-12 years old
● Can be benign or malignant
● Rarely causes secondary glaucoma, hyphema, ectopia lentis
● Pathology shows ribbons and cords of primitive round and oval cells,
multiple layers of neuroepithelial tables lined by thin basement
membrane; mucinous cysts and Flexner-Wintersteiner rosettes
● Can be seen in the retina and optic nerve
● B scan shows large cysts
● Treatment: observation or enucleation before orbital invasion (do not
resect as it induces metastatic spread)
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